Acquired combined immunodeficiency associated with protein losing enteropathy complicating Fontan operation.
نویسندگان
چکیده
It is vitally important that the immunological aspect of protein losing enteropathy following Fontan procedures is highlighted, in order to decrease significant morbidity and mortality
منابع مشابه
Protein-losing enteropathy after the Fontan operation.
Patients were observed after the Fontan operation to determine the frequency and severity of protein-losing enteropathy. A total of 427 patients who survived for 30 days after the Fontan operation, performed between 1973 and January 1987, were analyzed and, thus far, protein-losing enteropathy has developed in 47 of 427. The cumulative risk for the development of protein-losing enteropathy by 1...
متن کاملDiagnosis, treatment, and long-term follow up of a patient with a hydatid cyst of the left ventricle.
1 Hill D, Feldt R, Porter C, Puga F, Danielson G, Perrault J. Protein-losing enteropathy after Fontan operation: a preliminary report. Circulation 1989;80(suppl II):490. 2 Rothman A, Snyder J. Protein-losing enteropathy following the Fontan operation: resolution with prednisone therapy. Am HeartJ 1991;121:618-619. 3 Rychick J, Piccoli DA, Barber G. Usefulness of corticosteroid therapy for prote...
متن کاملCorrection: Protein-losing enteropathy in patients with Fontan circulation: is it triggered by infection?
Reference 1. Lenz D, Hambsch J, Schneider P, Häusler HJ, Sauer U, Hess J, Tárnok A: Protein-losing enteropathy in patients with Fontan circulation: is it triggered by infection? Crit Care 2003 7:185190. Correction Correction: Protein-losing enteropathy in patients with Fontan circulation: is it triggered by infection? Dominik Lenz1, Jörg Hambsch2, Peter Schneider3, Hans-Jürgen Häusler2, Ursula ...
متن کاملCASE STUDY Reversal of protein losing enteropathy with prednisone in adults with modified Fontan operations: long term palliation or bridge to cardiac transplantation?
Protein losing enteropathy (PLE), defined as severe loss of serum protein into the intestine, occurs in 4–13% of patients after the Fontan procedure and carries a dismal prognosis with a five year survival between 46% and 59%. Chronically raised systemic venous pressure is thought to be responsible for the development of PLE in these patients, with perhaps superimposed immunological or inflamma...
متن کاملClinical outcomes and improved survival in patients with protein-losing enteropathy after the Fontan operation.
BACKGROUND Patients with protein-losing enteropathy (PLE) following the Fontan operation have a reported 50% mortality at 5 years after diagnosis. OBJECTIVES The aim of this study was to review outcomes in patients with PLE following the Fontan operation. METHODS From 1992 to 2010, 42 patients (55% male) with PLE following the Fontan operation were identified from clinical databases at the ...
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ورودعنوان ژورنال:
- Heart
دوره 89 10 شماره
صفحات -
تاریخ انتشار 2003